Vascular Anomaly Related Syndromes

1. Klippel-Trenaunay Syndrome(KTS)
The K-T syndrome is a rare congenital malformation that may include the following: (1)Port-wine stain or "birthmark" (cutaneous capillary malformations),(2)Soft tissue and bony hypertrophy (excessive growth of the soft tissue and /or bones) ,(3)Venous malformations & lymphatic abnormalities.Complications may include bleeding, cellulitis, venous thrombosis, or pulmonary embolism. Associated abnormalities in other systems, such as gigantism of toes, hand and feet anomalies, lymphedema, or involvement of the abdominal and pelvic organs may also occur.

K-T usually is limited to one limb, but may occur in multiple limbs and/or head or trunk area. Internal organs may be involved. Each case of K-T is unique and may exhibit the above characteristics to differing degrees.

Terminology
The medical community at times has used the terms Klippel-Trenaunay Syndrome and Klippel-Trenaunay-Weber Syndrome interchangeably. The consensus today is to distinguish K-T as hypertrophy and varicosity associated with port-wine staining; K-T-W ( more co

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